IgG4-related disease of the hepatobiliary tract : 2 case reports and review of the literature
| Journal | Volume 81 - 2018 |
| Issue | Fasc.1 - Case reports |
| Author(s) | J. Spapen, A. Reekmans, B. Berghmans, S. Debeuckelaere, P. Buydens, L. Trappeniers, B. Van den Bossche, I. Colle |
| Full article |
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| (1) Department of Internal Medicine, Universitair Ziekenhuis Brussel, Vrije Universiteit Brussel, Brussels, Belgium ; (2) Department of Gastroenterology and Hepatology, Algemeen Stedelijk Ziekenhuis, Aalst, Belgium ; (3) Department of Radiology, Algemeen Stedelijk Ziekenhuis, Aalst, Belgium ; (4) Department of Abdominal and Hepato- Pancreatico-Biliary Surgery, Algemeen Stedelijk Ziekenhuis, Aalst, Belgium. |
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IgG4-related disease is a rare inflammatory disorder that may mimic many infectious, malignant, and autoimmune conditions. The biliary tract is frequently involved, but hepatic lesions are rarely seen. Diagnosis is often delayed due to the absence of specific clinical and radiological signs, and the lack of an accurate diagnostic marker. Differential diagnosis includes cholangiocarcinoma, primary sclerosing cholangitis and intrinsic or metastatic liver disease. Corticosteroids are the cornerstone of therapy but treatment has not been standardized and relapse is common. Based on two cases of IgG4-related hepatobiliary disease, we review the current literature on this pathological entity. (Acta gastroenterol. belg., 2018, 81, 83-87). |
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© Acta Gastro-Enterologica Belgica. PMID 29562380 |
